I loko o kahi kino maikaʻi, hele malū ka bile i ka 12-colon no kaʻaiʻana i kaʻai. I keʻano o nā maʻi i ke kūʻana, ka hoʻokaʻawale a me ka maikaʻi o ka wai olaola, hoʻomaka nā cholestasis -ʻo nā hōʻailona o kēia hilinaʻi ma muli o kona ikaika, a me kahi pūnaewele kahi i hanaʻia ai ka hopena.
Loaʻa i ka maʻi o ka maʻi kīpē kino a me ka hemohepatic. ʻO kaʻano mua e pili ana i kahi hana i ka synthesis o bile a me kona komoʻana i nā capillaries bile. ʻO keʻano o keʻano o ka maʻi e hōʻikeʻia ana e ke kaulike o ka'ōnaehana bile a iʻole e hoʻololi i ko lākouʻano.
Nā hōʻailona o ka maʻi cholestesis hepatic
Nā hōʻikeʻike nui o keʻano:
- Xanthomas a me xanthelasms. Ma luna o kaʻili he mea pālahalaha paha, he kīʻuʻuku paha, heʻano liʻiliʻi paha, he hueʻeleʻele. Hoʻonohonohoʻia lākou, ma keʻano he kūlana, ma nā puʻu, ka'ā'ī, ka hope a me ka umauma. I kekahi manawa, loaʻa nā xanthomas ma lalo o nā moma momona, ma nā poho o nā lāʻau.
- ʻO Steatorrhoea a me Acholia feces. Ma muli o ka uhakiʻana i ke kahe o ka bile, a me ka hoʻonaniʻana i loko o ka'ōpū liʻiliʻi o ka pūpū lipid, e lilo i mea hoʻonani i nā manu fecal a lilo i hinu.
- Ka'ōʻeleʻele o ka mimi. ʻO ka nui o ka bilirubin i loko o ke koko e alakaʻi aku ai i ka hoʻonui nuiʻana i loko o ka mimi, no ka mea i loaʻa iā ia he aka o kaʻeleʻeleʻeleʻele a iʻole ka pia pouli.
ʻO kekahi o nā hōʻailona maʻamau i nā cholestesis,ʻo ia kaʻiliʻana o kaʻili, me ka hopena o ka hopena o ke aʻalolo me ka waikeli bale. ʻOiai, he hōʻailona kēia i mua o jaundice.
Hiki i nā kūlana i lalo ke kūlike me nā maʻi pilikino:
- hawīmatoid arthritis;
- ʻO ka maʻi o Sjogren;
- nā meaʻai a me nā meaʻai lāʻau lapaʻau;
- 'ōniu;
- hepatic osteodystrophy;
- ka maʻi hemorrhagic;
- hihihihihihihihi ;
- polyneuropathy'ōpili;
- kāpili lāʻau ataxia;
- ka liʻiliʻi o ka retina;
- ʻo ka lawaʻole o ka maʻi hepic-cell.
Nā hōʻaia o nā cholestasis extrahepatic
ʻO nāʻanoʻelua o ke maʻi ua aneane like like ia, no laila e hoʻokumu i ka hōʻailona pololei i loko o ka papahana hoʻokolohua
ʻO nā hōʻailona kūikawā o nā cholestesis ma waho o ke ake a he:
- pinepine biliary colic;
- nā hōʻailona o cholangitis ;
- ka hopena o nā pancreatitis;
- holomua a kū like paha o ka pruritus me ka jaundice;
- ka pukaʻole o ka ate;
- ka holomua o ka maʻi maʻi.