Ma waena o nā maʻi maʻamau i uluʻia e ka hanauna,ʻo cystic fibrosis o nā māmā i ke poʻo o ka papa inoa. ʻO kēia pilikino pili i pili i ka uhaʻiʻana i ke kūlike o ka mea hūnā i hūnāʻia e nā'ōpū o loko, e hiki ai i ka hopena o ka'ōpū hanu a me ka'āpana o ka'ōpū.
ʻO ka maʻi kupa o cystic fibrosis
ʻO ka maʻi i nīnauʻia ka inoaʻo cystic fibrosis. ʻO keʻano o ka māmā kiʻekiʻe a me ka viscosity kaha o ke kīpili, kahi e uhi ai i nā kino kūlohelohe. No ka hopena o kēia kaʻina hana, ka hoʻohemoʻana i nā meaʻeleʻele, a me ka huakiko pathogenic e hoʻonui ai i ka līlū.
ʻO ka fibrosis pūpū o ka'ōpū he kumu hoʻokahi - e hōʻeha i kaʻehiku o ka chromosome (lima lōʻihi). Wahi a nāʻikepili,ʻo ka mea lawe i kēia maʻi,ʻo ia kēlā me kēia iwakālua ma ka honua. ʻO ka likelika o ka maʻi he 25%, akā inā he mauʻeha nā mākua.
Aiaʻekolu mauʻano o kēia maʻi:
- Cystic fibrosis ma ke kino;
- ka pulmonary a iʻole ka hanu hauhā cystic fibrosis;
- ʻano like (pulmonary cystic fibrosis).
ʻO ka fibrosis pūpū o nā mumū - nā hōʻailona
ʻO nā hōʻailona nui o ka maʻi:
- ka hoʻonāukiuki o ka viscous, ka wāʻeleʻele i ka wā o ka ulu;
- ka pinepine pinepine o ka niuʻona, bronchitis, pneumonia;
- ka hōʻehaʻehaʻana o ka'ōpū;
- maʻi maʻi;
- ka eha, ke kaumaha ma ka'ōpū;
- ka nui o kaʻaiʻana me ke kaumahaʻole a me ka hoʻolālā kino;
- nā moekolohe;
- pancreatitis ;
- ka nui o nā manamana lima ma nā lima;
- maʻi maʻi;
- maʻi diabetes;
- popoʻi ;
- ka momona o nā iwi;
- ka pāʻoiho o ka'ōpū (pololei).
Ke hōʻikeʻia ka'ōpala pulmonary o cystic fibrosis i loko o nā makahikiʻelua o ke ola, uaʻikeʻia e ka nui o ka'ikeleho i ka'ōpū waena a me ka liʻiliʻi o ke keiki.
Cystic Fibrosis - Keʻikepili a me kaʻike
Ua hanaʻia kaʻikepili me nā koho nuiʻehā.
ʻO ka mea mua, ua nānāʻia ke kūʻana o ka lā iʻeha i nā mākua a me nā hihia o ka uluʻana i loko o kaʻohana. ʻO nā hopena kūpono, a me kaʻike o ka hana hoʻomau i nā maʻi maʻamau i loko o ka maʻi a me ka bronchi, i mua o ka maʻi o ka'ōpū, ke kumu no ka ho'āʻoʻana i kahi wela. Aia ia i kaʻikeʻana i ke kiʻekiʻe o nā paʻakai i loko o ka wai i hoʻokuʻuʻia e nā pores. No ke kaʻina hana, he wahi liʻiliʻi ma ka lima (ma luna o ka kuʻe lima) e mālamaʻia me kahi lāʻau lapaʻau i kapaʻiaʻo pilocarpine. Hoʻopiliʻia kekahi electrode i kēia'āpana, e hoʻonāukiuki ana i ka hoʻokuʻuʻana o ka wela, i hoʻokaʻawaleʻia e ka mea ulaula a me nā mea paʻahana wela, e hana ana i ka hopena o ka sauna. Ma hope o 40 mau minuke, hiki ke hoʻopiliʻia ka wai i ka paʻakai paʻakai. Inā piʻi ka pae i nā palena palena, ua hanaʻia kahi hopena hope loa.
ʻO ka fibrosis pūpū o ka'ōpū - ka lāʻau
ʻO keʻano o ka maʻiʻaʻole ia e lapaʻau loa ia, ua hoʻohanaʻia ka curerapy i ka hoʻohemoʻiaʻana o nā hōʻailona a koiʻia he ala i integrated. Hanaʻia nāʻano hana e like me kēia:
- nā lōʻihi o nā lāʻau'alopelo;
- nā kālepa hoʻokipa;
- kinesitherapy;
- Ka hoʻomohuʻana i nā hormones corticosteroid a me nā mimetics beta;
- hoʻohana i ka bronchodilator;
- hana i nā'ōlohelohe;
- ka hoʻoponoponoʻana i kaʻai me ka piʻiʻana o ka uku manawa o 10-15%;
- nā hoʻowaiwai pū'āwai lele;
- ka pākani;
- ka loaʻaʻana o nā huaora a me nā microelements.
ʻO ka'ōlaula a me ka maikaʻi loa i ka manawa o keʻano o ka lāʻau lapaʻau ka transplantation o ka pulupulu. Eia hou, ke hoʻomau mauʻia nei ka noiʻi hoʻomōʻai no ka hoʻoponoponoʻana i ka pūpū i hōʻinoʻia e nā hanaʻino i hanaʻia.