ʻO ka meaʻaiʻole maikaʻi, ke ola i loko o ka pilikia, ka paʻakikī o ke kaiapuni -ʻo kēia mau mea e pili ana i ke olakino o kekahi kanakaʻaʻole no ka maikaʻi. ʻO ka hopena, ua ulu pinepineʻia ka maʻi i hanaʻia e ka'ōnaehana ma ke kino. ʻO kēia mau mea he lāʻau'ōmimune (idiopathic) thrombocytopenia aʻo Verlhof paha.
Nāʻano a me nā kumu o ka thrombocytopenia autoimmune
ʻO kēia kahi maʻi maʻi koko, kahi e ho'ēmiʻia ai ka helu o nā platelets no ka meaʻo ka hoʻomakaʻana o ka ulumahu e hana i nā mea pale e kū'ē i kēia pūʻulu o nā pūnaewele. Hoʻopukaʻia ka thrombocytopenia maʻamau:
- mua,ʻo ia hoʻi, e puka ana i waho;
- secondary, manifestation as a result of the defeat of the immune system as a result of diseases such as cancer of the lymph nodes, HIV, rubella, autoimmune hepatitis, etc.
- ke lāʻau lapaʻau, i hanaʻia ma hope o ka laweʻana i ka lāʻau lapaʻau aiʻole nā lāʻau lapaʻau.
Nā hōʻailona o ka thrombocytopenia autoimmune
ʻO kahi hōʻailona o ka hoʻonuiʻana i kēia maʻi,ʻo ia keʻano o nā hemorrhages maha ma keʻano o nā mea liʻiliʻi. ʻO ka hapa nui o lākou ma kaʻili o ke kumu a me nā poʻo. Hiki ke hoʻomaka i nā hiʻiʻehā hemorrhagic. Eia kekahi, aia ka kahe o ka mucosa i loko o nā hale ākea a waha.
No ka mea he kuleana nā platelets no ke kāpiliʻia o ke koko,ʻo ia hoʻi me ka hōʻailona likeʻole, inā iʻinoʻino kaʻili, hikiʻole ke paniʻia ke koko. ʻO kēia kekahi e pili ana i ka nui o nā manawa diabolis o ka wahine, a ma ka feces ke koko.
Ināʻaʻole iʻikeʻia nā pilikia e hikiʻole ke hoʻopauʻia (e like me keʻano o ka hemorrhage āpau),ʻo ka lapaʻau kūpono no nā maʻi me ka thrombocytopenia autoimmune. ʻO ka maʻi ma ka mea hoʻokahi wale nō e hele ai, aiʻole ka hopena e loaʻa mai ma muli o ka mālamaʻana.
Hoʻomaʻoʻia o ka thrombocytopenia autoimmune
ʻO ka maʻamau nui no ka thrombocytopenia autoimmune ka mea e hoʻopau ai i ka hanaʻana o nā autoantibodies e'ānai ana i nā platelets, akā ma ka mea mua eʻikeʻia. No kēia mea, pono e waihoʻia kekahi mau ho'āʻo:
- he hōʻoia kokoʻana ;
- kaʻike nui o ka urine;
- ke hōʻoia e like me keʻano Steffen (hoʻoholo i ka nui o ka antiglobulins);
- Ka ho'āʻoʻana o Dickson (hōʻole hōʻole).
Me kahi mālie o ka thrombocytopenia autoimmune, ua kauʻia nā lāʻau'alomoni mai ka hui o glucocorticosteroids (ka nui o nā prednisolone i ka 1 mg per kg o ke kaumaha o ke kino). Lawe i ka mea e pono ai ke ola hou, a laila e ho'ēmi iho i ke kau. Ināʻaʻohe kōkua o ke kaola lāʻau, hana nā kauka i kahi hana e wehe i ka'ōpū.