ʻO nā vasculitis hemorrhagic i nā keiki

ʻO ka vascitis hemorrha o nā keiki, he maʻi ia e pili ana i nāʻili o kaʻili, a me nā kīʻaha koko o ka'ōpala pahū, nā hono a me nā'ōpū. Aia ia i ka hui o nā maʻi āpau āpau āpau o ka pilikino. ʻO ka hoʻomakaʻana o ka uluʻana o kēia maʻi e hiki ke hana ma nā makahiki, akā,ʻo keʻano,ʻo nā keiki'ōpiopio loa (hiki i 3 mau makahiki) pilikia loa i kēia maʻi.

ʻO ka hapanui o nā makahiki,ʻikeʻia nā vascitis i nā keiki 4 a 12 mau makahiki.

He nui nāʻano vasculitis hemorrha,ʻano'ē i ko lākou mauʻike a me keʻano. No laila, ua māheleʻia ka vasopathy i loko oʻelua mau lālā o waena: ka maʻi ola (Hippel-Landau maʻi, ka maʻi maʻi Ehlers-Danlo, ka maʻi maʻi Kazabaha-Merrita, Louis-Bar, a pēlā aku) a loaʻa (hōʻailonaʻia me nā allergies o nā kumu likeʻole, nā meaʻino, hypovitaminous a infectious vasopathies, a me nā mea'ē aʻe).

ʻO ka hemorrhagic Vasculitis: kumu

ʻO ka maʻi ke kumu o ka hōʻinoʻiaʻana o nā paia capillary a me ka piʻiʻana o ka holomua o nā moku a pau, a me ka hoʻouluʻana o ka pūnaehana kōkua a me ka hoʻonuiʻana i ka helu o nā māmā uila i hanaʻia.

ʻO ka hapanui o ka manawa, hoʻomaka ka uluʻana o ka maʻi i kekahi manawa ma hope o ka maʻiʻeha (ARVI, tonsillitis,ʻulaʻula, a pēlā aku). I kekahi manawa, ma mua o ka uluʻana o vascitis i kaʻaeʻana i ka lāʻau (a iʻole nāʻano likeʻole o nā mea hōʻailona), ka mīpīpikipiki, ka pākī a me ka maʻamau.

Nā hōʻailona o vasculitis i nā keiki

Ma ka hapanui o nā hihia,ʻo ka hōʻailona mua o ka maʻi,ʻo ia keʻano o kahi'ōpiopio liʻiliʻi o kaʻulaʻula. Ke kuʻi o ka huhū: nā pūpū o nā lālā, nā kīwae, a me nā wahi o nā hono. Hōʻaleʻa waleʻia ka helehelena ma nā maka, nā poho a me nā wāwae, ke kumu. Ma hope o ka halaʻana o ka'ōpala, e mau ana kahi o ka puaʻaʻeleʻele i kona wahi, kahi e hoʻomaka ai e pale aku me nā loli pinepine o ka maʻi.

ʻO ka hōʻailona maʻamau kaʻoi aku o ka hoʻohaunaele likeʻole. Hoʻomaopopoʻia mai ka hebedoma mua o ka maʻi. Hiki keʻokoʻa keʻano a me ka lōʻihi o kaʻeha,ʻo ka nui o nā hui nui,ʻo ia ka haʻalulu a me ke kuli. I kēia hihia, hiki i nā'ōpili hui, akāʻaʻoleʻaʻohe hoʻololi o ka hana a me nā maʻi o nā mea i hanaʻoleʻia.

ʻO ke kolu o ka hōʻailona maʻamau ka maʻi kaumaha. Hiki ke hōʻike me ka hōʻeha paha i kaʻili a me nā hono. Hiki i nāʻeha o kaʻeha ke hana pinepine i nā lā a pau, me kaʻole o ka localization. I ka manawa pinepine, mālamaʻia ka inu, ka luaʻi, a me ke kuni. I nā mea koʻikoʻi, hiki i ke kahe koko a me ke koko.

ʻO kekahi manawa me nā vasculitis haemorrha,ʻo nā pūpū a me nāʻano'ē aʻe (puluk, puʻuwai, nā moku lolo) e pili. ʻO ka paʻakikī o nā liona e hiki keʻano likeʻole - mai ke keiki liʻiliʻi, i ka hoʻohaʻahaʻa a me nā hihia koʻikoʻi.

ʻO ka vasculitis Hemorrhagic i nā keiki: ka lāʻau

ʻO keʻano a me nāʻano o ke olakino ma keʻano o ka hopena a me keʻano o ka maʻi (ka hihia mua, hoʻihoʻiʻia o ka manawa maʻi a iʻole manawa hoʻokuʻi), ma nā hōʻikeʻike a me ka paʻakikī, a me ka lōʻihi a me keʻano o ka maʻi. Akā, hiki ke kaʻawale i waho o keʻano maʻamau,ʻoihana maʻamau maʻamau.

No nāʻano a pau o ka maʻi, nā mea hana maʻalahi i hoʻohanaʻia. E hāʻawi i ka kurantil (persanthin, dipyridamole) i 4 mau manawa o ka lā ma ke alapine he 5-8 mg i ka kilokika o ke kaumaha o ke kino, ke ahupuaʻa (agapurine, pentoxifylline) 3 manawa i ke ao no ka 5-10 mg / kg ke kaumaha o ke kino. I nā hihia koʻikoʻi, hiki ke hoʻohanaʻia nāʻano lāʻauʻelua i ka manawa hoʻokahi. Hiki ke hoʻohālikelike ka lōʻihi o ke kaʻina hana - mai nā mahina 2 a 12, ma muli o ke koʻikoʻi o ka maʻi. I ka manawa maʻamau e hoʻonohonoho i nā papa hana manawa (ka hapahā a me nā mahinaʻeono).

Hoʻohanaʻia nā kuʻikahi-coagulants ma nā mea pono'ī, nā mea ho'āla o fibrinolysis, nā pūnaewele, glucocorticosteroids, nā stabilizers membrane, cytostatics, antihistamines. Hoʻomohanaʻia ka transfusion therapy a me plasmapheresis. ʻO ke kohoʻana o nā lāʻau lapaʻau a me nāʻano o ka lāʻau lapaʻau, pono e hanaʻia e nā kauka wale nō, hoʻoponopono pono'īʻia aiʻole ka hoʻonohonoho kūponoʻole o ka hōʻailona hana ma waho o ka nīnauʻana me nā kānaka lapaʻau a me ka nānāʻana i ke olakino.

ʻO ka paleʻana o vasculitis hemorrhagus

ʻO ka hana nui loa no ka paleʻana i ka maʻi,ʻo ia ka paleʻana, ka paleʻana i nā hana kūpilikiʻi o nā maʻi pīpīpili, ke kaʻawaleʻana mai nā mea mai. ʻAʻole hiki i nā maʻi ke hana i nā huapiʻi me nā antigens bacterial (ka ho'āʻoʻana i ke kīpau, ka tuberculin, a me nā mea'ē aʻe). No ka paleʻana i nā vasculitis hemorrha i loko o nā keiki, he hypoallergenic nui ia,ʻo ka mālamaʻana i ka meaʻai, kahiʻaiʻai maikaʻi a me kahi ola olakino.