ʻO ka maikaʻi maikaʻi

ʻO kēia maʻi ka mea i kapaʻia he maʻi pīpona pumeumona me nā nephritis, hemorrhage pulmonary a idiopathic hemosiderosis. ʻO kona inoa maoliʻo Goodpasture's Syndrome. He maʻi nui loa kēia e pili ana i hoʻokahi kanaka i ka miliona. Akā ponoʻoe eʻike e pili ana i kona mau hiʻohiʻona, nā hōʻailona a me nāʻano o ka hoʻomalu.

ʻO nā kumu nui a me nā hōʻailona o Goodpasture Syndrome

ʻO kēia ka maʻi liʻiliʻi maʻamau e pili ana i nā maʻi a me nā kēpau o nāʻano paʻakikī o ka alveoli pala. Ma keʻano'ē aʻe, e ulu ana ka maʻi i nā kānaka me ka maʻi palupalu a ma keʻano o ka hemorrhage pulmonary. ʻO ka maʻi i loaʻa i ka maʻi maikaʻi a me ka hapa nui o nā maʻi - nā'ōpio. ʻO ka maʻi i makemake i nā kāne ma waena o nā makahiki o 18 a 35.

Ua kākau nuiʻia nā hana'enekema a me nā puke ma Goodpasture's Syndrome, akāʻaʻole i hiki i kaʻepekema keʻike i ke kumu o kēia maʻi. Uaʻikeʻia heʻoiaʻiʻo ua kauʻia ka maʻi ma luna o ke kūkuluʻiaʻana o nā'elepona'elepili kūikawā, i ka hopena, e hoʻopili i nā mea hana paʻa i loko o ke kino. ʻO kēia mau hopena e hopena i ka pōʻino o ka pāpaʻi.

Loaʻa nā manaʻo i ka maʻi maikaʻi o Goodpasture e hiki ke hoʻopiliʻia e nā maʻi o ka viral a iʻoleʻo bacteria (e like me keʻano,ʻo ka maʻi pīnī). Ma waho aʻe, hiki i nā kumu o waho ke loaʻa ka hopena maikaʻiʻole i ka pūnaewele immune. E like me ka hōʻikeʻana, hōʻike pinepine pinepine nā mea'umeka mai ka ulupalaʻau i ka maʻi. ʻO nā pōpilikia a me nā kānaka e hana ana i loko o ka hale me kahi me nā mea hanaʻino, a me nā mea lawe i kekahi mau lāʻau, e hōʻikeʻia.

E noʻonoʻo ana i nā kumu o ka maʻi,ʻaʻole mākou e hoʻopoina e pili ana i ka predisposition genetic, akā ma ka hihia o Goodpasture's Syndrome, pono paha kēia hewa. Aʻo kekahi poʻe akamai a ke manaʻoʻiʻo nei lākou e ulu ana kēia maʻi ma muli o ke kūlana o ka mīpīpī.

ʻO nā hōʻailona mua o Goodpasture's Syndrome e like me nā hōʻailona o nā maʻi o ka lolokia. ʻO ka hiʻohiʻonaʻike nui ke holo wikiwiki. ʻO ka likeʻole o ke anu maʻamau, maikaʻi ka maʻi o Goodpasture mai ka mua a hiki i kahiʻoihana nui loa i hikiʻole ke hoʻomau i nā lā.

ʻO nā hōʻike nui o kēia maʻi:

Ka hōʻailona a me ka mālamaʻana i ka maʻi o Goodpasture

Ināʻaʻoleʻoe e hoʻolohe i ka maʻi o Goodpasture, hiki i ka maʻi ke alakaʻi i ka make. I mea e pale ai i ka lōʻihi a me ka maʻalahi paʻakikī, me nā manaʻo mua e makemakeʻia e nīnau i kekahi limahana. ʻO ka diagnose hiki i ka maʻi ke hōʻoia i ka hoʻokolokolo piha.

Ma ke koko o ka mea hoʻomanawanui, hiki i ka hoʻonaʻauao ke hoʻoholo i ka hikiʻana o nā'elepona kūikawā. Eia hou, hiki i ka haʻalulu ke hoʻoulu i ka hemoglobin a me nā kiʻekiʻe kiʻekiʻe o nā pūpū koko keʻokeʻo. Ma ka ho'āʻoʻana i ke koko no ka maʻi o Goodpasture e hōʻike i ka nui o ka meaola. Ma kahi o ka roententogram eʻike maopopoʻia nā wahi hoʻolino.

ʻO keʻano o ka hōʻailona o ka maʻi o ka maʻi maikaʻi ma kahi o ka wā mua e ikaika. ʻO ka manawa maʻamau,ʻo ia nō nā hōʻailona hormonal a me nā istiostatics. Ponoʻia kekahi mau maʻi e hōʻike i keʻano hoʻohālike - transfusion o ka plasma a me ka mass erythrocyte. Inā hoʻonāʻia ka maʻiʻekeʻeke i kahi hana hoʻokipa haʻahaʻa, dialysis, a i kekahi manawa kekahi mea e kanu ai.