He nui loa nāʻano pilikino pūnaewele, aʻo ka hapa nui o nā kānakaʻaʻoleʻike i kekahi mea e pili ana iā lākou. ʻO kekahi o kēia mau diagnoses he vasculitis - he aha iaʻano maʻi, he aha kona mau hōʻailona, nā hopena a me nā koho hoʻoponopono no nā mea maʻi iʻikeʻoleʻia. No laila, ma mua o ka hoʻomakaʻana o ke olakino, ke alakaʻi nei ka mea kauka he kūkākūkā kūkākūkā me ka hoʻokomo ponoʻana o ke kauka olakino, no ka mea,ʻo ka pathogenesis o ka pūnaewele palekana ke kino o ka maʻi.
He aha kēia maʻi "vasculitis", a he aha kona mau hōʻailona?
ʻO ka maʻi i hōʻikeʻia he hōʻuluʻulu o nā maʻi i hoʻohuiʻia i kahi hana maʻamau o ka maʻi - ka hūʻana o nā paia o nā'enela, capillaries, venules, arterioles a veins. ʻO kaʻoiaʻiʻo,ʻo ka vasculitis he maʻi o nā kīʻaha koko a me ke koko e hele mai ana i loko o lākou i nā mea lewa a me nā ohe e pili ana i nā hoʻololi a me nā hoʻololi.
Ka hoʻohālikelikeʻana i ka maʻi:
- ʻO ka vasculitis mua ka hopena o nā kīʻaha koko i hāpaiʻia no nā kumuʻikeʻole.
- ʻO keʻanoʻelua o ka maʻi vasopitis - nā maʻiʻeleʻele iʻikeʻia i ka paneʻana i kekahi mau maʻi pūnaewele.
I loko o ka lāʻau lapaʻau, ua heluʻia ka maʻi i nīnauʻia penei:
1. Nā Vasculitis o nā moku liʻiliʻi:
- Ka maʻi o Charge-Strauss a iʻole eosinophilic granulomatosis me polyangiitis;
- pāʻokoʻa anti-GBM;
- Cryoglobulinemic vasculitis;
- ʻO ka maʻi o Wegener a iʻole granulomatosis me polyangiitis;
- ʻO Immunoglobulin-A-vasculitis a me nā meaʻulaʻula Shonlein-Genocha;
- ka anti-C1q-vasculitis a iʻole maʻi hypocomplexary urticaria;
- ka polyangiitis microscopic.
2. Nā Vasculitis o nā mokuhana pili:
- nodular periarteritis aiʻole polyarteritis nodular;
- Kapalaaki maʻi .
3. Vasculitis o nā moku nui:
- o Takayasu;
- ʻO ka maʻi o Horton a iʻole keʻano o ka hoʻopaʻaʻana i ke kepau.
4. Nā vasculitis o nā moku likeʻole:
- Koʻo maʻi o Kogan;
- ʻO ka maʻi o Behcet.
5. Vasculitis o nā'ōpuni:
- ʻokiʻoki;
- ka mua angiitis o ke kikowaena pūnaewele;
- ʻokoʻa aortitis;
- lekicocytoclastic'ā'ī angiitis a me nā mea'ē aʻe.
6. Nānāʻau pūnaewele:
- rheumatoid;
- lupus;
- sarcoidosis a me nā mea'ē aʻe.
7. Nānā vascularitis lua:
- pili pū me nā mea maʻi;
- 'ōpala;
- pili i nā lāʻau lapaʻau a me nā mea'ē aʻe.
Nā hōʻailona maʻamau o ka maʻi pilikino:
- piʻi kiʻekiʻe;
- pallor;
- luhi;
- nele i kaʻona;
- nāwaliwali.
ʻO ke kūlana o ka maʻi o vascularitis e pili ana i konaʻano, nā'ōpuni a me nā pūnaewele i pili, ka nui o ka mumū a me nā kumu'ē aʻe. No laila, hiki i kahi kauka ke hōʻoia i ke ahulau ma muli o keʻano o nā hoʻokolohua physiological, nā hoʻokolohua labo laboratory, a me nā haʻawina hana.
He aha keʻano o kēia maʻiʻehā?
E like me ka inoa e hōʻikeʻia ana,ʻo ka hōʻailona o keʻano o ka hōʻailona,ʻo ia ka hoʻomāmā o nā kīʻaha koko e pili ana i ka hopena o ka hopena maʻi. ʻO kona kumu nui - kaʻili o ke kino, kahi e likeʻole ai konaʻano. E like me ia, uaʻikeʻia nā vasculitis mai ka maʻi he maʻi'ē aʻe, ua hoʻohuiʻia lākou i nāʻano like:
- erythema nodosum - kaʻike o nā hōʻailona ma lalo o kaʻili o ka mālamalama;
- Arteriolitis Rutera - ka'āpala i keʻano o ka papules, nā kikooho, "hōkū", nāʻano i hui pū me ka olakino maikaʻi;
- ʻo ka vascularitis hemorrhagic -ʻaʻole iʻikeʻoleʻia nā hōʻailona me kēia maʻi,ʻaʻole iʻikeʻia, loaʻa mauʻia i ka dopplerography (i loko o nā moku he microthrombi);
- hemosiderosis - keʻano o ka poniʻalani-brown-brown i kaʻili;
- necrotizing vascularitis - ka make mālie o kaʻiʻo ma hope o ka hoʻomakaʻana o ka epidermis rash.
He aha kēia maʻi "wīpīmatoid vasculitis"?
ʻO kēiaʻano maʻi pilikino heʻano ia o ka hoʻolālā pūnaewele lua o nā paia pāpuni, e ulu ana ma muli o ka piʻiʻana o ka maʻi o ka'ōhumu.
Uaʻikeʻiaʻo kēiaʻano vascitis ka mea e pilikino ai i ka maʻi o nā mumū, nā pūpūʻeha, kaʻili a me kaʻili o ke kui, ka maʻiʻole (pericarditis). Eia naʻe, uaʻikeʻia nā hōʻailona maikaʻi o ka maʻi ma lalo o ka 1% o nā maʻi, no laila uaʻikeʻia keʻano o keʻano o ka maʻiʻeleʻele i ka wā i hala, a he mea paʻakikī ke mālamaʻana i nā maʻi āpau a me nā vascitis.