Lymphogranulomatosis - hōʻailona

ʻO ka Lymphogranulomatosis e pili ana i ka uluʻana o ka maʻi kino, e hele pū me ka hopena o nā pū hematopoietic i loko o nā pūnana lymph a me nā mea likeʻole. ʻO ka hopena i ka uluʻana o ka maʻi,ʻo ia ka hoʻololiʻana o kahi non-rover cell e pili ana i ka maʻi, ka radiation radioactive a iʻole ke kūkāʻana me kahi mea hana kino, akāʻaʻole maopopo nā kumu o ka lymphogranulomatosis a hiki i ka hopena. ʻO keʻano nui o ka hana a nā kauka i keʻano o ka maʻi viral o ka maʻi,ʻo ia hoʻi, pili i ka maʻi Epstein-Barr.

Nā hōʻailona o ka lymphogranulomatosis

I nā papa mua, ua loaʻa maikaʻiʻole ke maʻi, aʻo ka mea wale nō e hiki ke hoʻohuli i ka manaʻo o ka mea maʻi ke piʻiʻana o ka'īlio lymph, aʻo ka lōkahi o iaʻano heʻino. ʻO ka hapanui o nā māmā lymph ma ka'ā'ī e kū mua i ka'ā'ī, akā ma kekahi mauʻano, e komo mua nā aʻa o ka mediastinum, nā'ahuʻula a me ke kiko; he mea mau loa - he mau hope retroperitoneal.

ʻAʻole i hele pūʻia ka hōʻailona o ka'īlio lymph nui me nāʻanoʻeha. Hoʻopiʻiʻia kahi meaʻeleʻele,'āwili i ka mea, a ma hope aku lilo i maʻalahi a emiʻole ka pūnaewele.

Ke lohe nei i ka hōʻailona o lymphogranulomatosis, hikiʻole i kekahi ke hāʻule i kahi hōʻailona nui e like me ke kiʻekiʻe o ke kino o ka kino, kahi hikiʻole ke kiolaʻia i lalo e Aspirina,ʻAmelika, aiʻole mau lāʻau'alope. ʻO ka hapanui pinepine, ke hoʻomaka ka wela i ka pō a ua hele pū me ka lohi kaumaha, me kaʻaʻohe puʻu.

I loko o 30% o nā hihia,ʻo ka hōʻailona mua o lymphogranulomatosis kaʻiliʻeleʻele,ʻaʻohe hiki ke hoʻoneʻeʻia e kekahi mea.

Eia kekahi, ke hoʻopiʻi nei nā mea maʻi i kaʻeha ma ke poʻo, nā hono, hoʻemiʻia ka makemake, ka luhi. Aia kahi kaumaha kaumaha.

ʻIke i ka lymphogranulomatosis

Ma muli o ka hoʻopiʻi o ka mea maʻi e pili ana i ka wela a me ka'īpili waipili nui i kekahi hapa o ke kino, hiki ke kauka i ke kauka lymphogranulomatosis, aʻo ka ho'āʻoʻana i ke koko e kōkua pono e hoʻololi i nā hōʻailona. No laila, i loko o ka hale hoʻokolohua, leukocytosis neutrophilic, lymphocytopenia pili aiʻole paʻa paha, uaʻikeʻia ka nui o ka lolemai erythrocyte. ʻO nā pākākūkā i nā papa mua o ka maʻi,ʻo ia keʻano maʻamau, he maʻamau.

ʻO nāʻike hou e pili ana i ka hopena o ka puka i hahau muaʻia. I loko o kahi biopsy, uaʻikeʻia nā pūnaewele kaulanaʻo Reed-Berezovsky-Sternberg a me / aʻo nā pūnaewele Hodgkin. Hana lākou i nā kani o nā mea i loko a me ka biopsy o ka iwi.

Ka hopena o ka maʻi a me ka hōʻailona

Ma waho aʻe o nā kōpili lymph,ʻo ka maʻi ma kekahi mau mea e pili ana i ka'ōpū, nā mumū, ka ate, ka momona o ka iwi, nā pūpū nervous, nā puʻupaʻa. E kū'ē i ka hope o ka hoʻonāwaliwali o ka palekana, nā maʻi, a me nā maʻi viral i ulu, e hiki ke lilo iʻoi aku kaʻino ma hope o ka hoʻokalahalaʻana a me ka chemotherapy . Hoʻopaʻa pinepineʻia:

ʻEhā lālani o lymphogranulomatosis:

  1. ʻO ka'ōpū e waiho waleʻia ana ma loko o nā lymph nodes a iʻole ma waho o lākou i hoʻokahi pū hoʻokahi.
  2. ʻO ke koko e pili ana i nā puka lymph ma nā wahi he nui.
  3. Ke hele nei ka maʻi i nā puka lymph ma nāʻaoʻaoʻelua o ka diaphragm, ua pili ka manu.
  4. Hiki i ka'ōpū ke pili i ke ake, a me nā'ōpū a me nā mea'ē aʻe.

Ma keʻano he lāʻau hoʻomalu no ka lymphogranulomatosis, hoʻohanaʻia ka chemotherapy me ka radiotherapy a iʻole. Eia kekahi, he meaʻaeʻaʻia keʻano o ka lāʻauʻana me nā wela nui o nā lāʻau lapaʻau lāʻau liʻiliʻi, a ma hope iho ua kāpiliʻia ka mea maʻi i ka momona o ka iwi.

No ke ola o ka nohoʻana o lymphogranulomatosis,ʻo ka hāʻawiʻana i kahi hoʻomalu i 10 a 20 mau makahiki i 90% o nā maʻi, he helu kiʻekiʻe. I loko o nā hopena hope loa o ka maʻi, ua hāʻawiʻia ke kaʻina o nā mea maʻamau i 80% o nā hihia 5 mau makahiki o ke kala.