ʻO ka maʻi maʻi o Behcet he maʻi maʻi hou loa,ʻo ia ka maʻi maʻamau i Iapana a me nā moku'āinaʻo Mediterranean. ʻO ka hapa nui o ka uluʻana o ka poʻe makahiki 30 - 40 mau makahiki. ʻO kēia maʻi i pili i ka hui vascitis a he'ōlelo hoʻokaheʻole.
Nā kumu o ka maʻi o Behcet
ʻO ka uluʻana o ka maʻi i hoʻohuiʻia me kekahi mau kumu kūikawā, a eia nā mea penei:
- ka predisposition genetic;
- herpes a me ka maʻi streptococcal ;
- kumu helu autoimmune.
Manaʻo ka hapanui o nā kānaka i ka hopena o ka maʻi o Behçet e hoʻonāukiukiʻia e nā hopena o ka pilikia, a ma ka wā e hiki mai ana, ua pili nā pūnaewele autoimmune iā lākou, akā, e hoʻolako i nāʻano hana predisposition.
Nā hōʻailona o ka maʻi o Behcet i nā wāhine
ʻO kēia maʻi i hōʻikeʻia e polysimptomicity. I kēia hihia,ʻo nā hōʻailona nui, kahi e hiki ai iāʻoe ke hana pololei i ka hōʻailona, ke pili pū me nā meaʻino i nā membpa mucous o ka waha a me nā genitals, a me nā hanaʻeleʻele i nā maka. E noʻonoʻo i nā hōʻailona a pau o ka maʻi o Behçet ma keʻano kiko'ī.
Ka pōʻino waha o ka waha
I ka hoʻomakaʻana,ʻikeʻia nā mea liʻiliʻi me nā meaʻeleʻele i nā lehelehe, ka lani, ke alelo, nā'āpala, pharynx, kaʻaoʻao o nā papalina, a laila weheʻia. Ma kahi o nā vesicles, ākea, ua hanaʻia nāʻehaʻeleʻele'āpana (aphthae) o ka'ōniʻomaʻoʻulaʻula'ōmaʻomaʻo,ʻo ka nui o ia mea e hiki ke piʻi i 2 knm ke anawaena. ʻO ka ho'ōlaʻana i nā maʻi hee ma kahi o ka mahina ma hope aku, me ka manawaʻekolu o ka makahiki e hoʻi hou ka leona.
Nā maʻiʻeha
ʻO nā wāhine ma ka membrane mucous o ka pēina a me nā maʻiʻeleʻele, he mau meaʻeha, e like me nā mea i loko o ka waha. Ma hope o ka ho'ōlaʻana, e mau ana nā wī ma ko lākou wahi.
Nā meaʻino o ka hihi
Hōʻikeʻia kēia mauʻike he mau pule ma hope o ka hōʻailona ma ka waha waha. Hiki i nā maʻi ke hoʻoulu i ka mumunui o ka iris a me ka maʻi ciliary o ka'ōpū, ka līʻana o nā membpa vascular a mucous o ka maka, ka wela o ka'ā'ī. ʻO ka manawa pinepine nā hōʻailona o kēia mau mea: photophobia, iʻikeʻia ka hihiʻo, hoʻonuiʻia ka lacrimation.
Nā hōʻikeʻoki
Nodular erythema, pyoderma, paulo-vesicular push paha. Eia kekahi ma kekahi mau hihia, e mālamaʻia nā poho o ka lauoho poho, ka panaritium ma lalo.
Nā maʻi o ka pūnaewele musculoskeletal
Aia ke uluʻana o ka maʻi o ka maʻi (he mau haʻahaʻa haʻahaʻa wale nō) me nā mea hoʻopauʻole.
Nā hōʻailona neuropie
Aia kekahi mau hanana o nāʻeha o ke kino o ke kino, ka hoʻomōhalaʻana i ka maningoencephalitis, ka edema o ka'ōpae nerve opic, keʻano o hemiparesis.
ʻO nā loli o kaʻikepili āpau
ʻO keʻano o ka uluʻana o vasculitis, thrombophlebitis o nā veins ma ka wāwae, ka thrombosis o nā maʻi hepatic a me ka thromboembolism o ka armonia pulmonary, aoric aneurysm, etc.
Me nāʻeha o ka'ōpū hanuhinu, ka naʻau a me ke akemāmā, aia paha i nā hōʻailona:
- nausea;
- ka wele;
- hemoptysis;
- ka eha i loko o ka puʻuwai, a pēlā aku.
Hanaʻia o ka maʻi o Behcet
ʻO ka hoʻomaluʻana i ka maʻi o Behcet, ma mua, he mea nui e hoʻonui i ka ola o ka mea maʻi, e loaʻa i ka hoʻomaha pinepine a pale i nā loli hikiʻole ke hoʻololi i nā'ōpū o loko.
Hōʻikeʻia nā hōʻailona o ka Behcet's Syndrome i loko o ke ākea waha a ma luna o nā genitals e mālama i ka lāʻau me ka hoʻohanaʻana i nā glucocorticosteroids , nā antiseptic solutions, a i kekahi manawa - nā mea āpau antipodal. A no ka hoʻomaʻamaʻaʻana i ka maʻi, nā mea hana cytostatic, immunosuppressors, hiki ke kauʻia nā huaora. Hoʻopilikiaʻia kaʻinoʻino ma nāʻano kālaihana. Hoʻopaʻaʻia he mau maʻi he nui no ka hemocorrection hemo. Hoʻoponoponoʻia ke kaulike ma lalo o ka mālama olakino.