Ma keʻano he kūlana, hiki keʻike i ka cystic fibrosis i ka wā'ōpiopio, no ka mea, uaʻikeʻia keʻano o kahi hōʻailonaʻano maikaʻi loa. Akā, ma ka hōʻoluʻolu a hoʻonuiʻana i keʻano o kahiʻanoʻano likeʻole,ʻikeʻia kēia maʻi ma kahi maikaʻiʻole. No laila, he mea nui eʻike, i mea eʻike ai i nā maʻi likeʻole e like me cystic fibrosis - nā hōʻailona a me nā hōʻailona o waho.
ʻO ka maʻi o cystic fibrosis - he aha ia?
ʻO ke maʻi i nīnauʻia,ʻo ia, he hōʻailona. Kū mai ia mai ka hoʻololiʻiaʻana o kahi pūnaewele e waihoʻia ma ka lima lōʻihi o ka chromosomeʻehiku. ʻO ka maʻi o ka maʻi inā wale nō inā e halihali ana nā mākuaʻelua i ka mea i hōʻinoʻia, a he 25%. Me kēia mau kumu,ʻo ka maʻi o cystic fibrosis e pili ana i ka nui o nā kānaka, no ka mea, aia kahi chromosome me ka hoʻololiʻana i kēlā me kēia 20 o ka noho ma ka honua.
ʻO ke kaupili pa'ū i nā mākua - hōʻailona
E like me ka mea iʻike muaʻia,ʻikeʻia ka maʻi i loko o ka'ōpiopio, hiki i ka 2 mau makahiki, a he 10% wale nō o nā maʻi i loaʻa nā hōʻailona mua ma ka'ōpiopio a me ke kino.
ʻO nā hōʻailona nui o cystic fibrosis:
- lag i ke kākoʻoʻana o ke kino, aʻo nā noʻonoʻo kūpono he mea maʻamau aʻoi paha ma mua o ka mea maʻamau;
- ka lahilahi o nā manamana lima ma ka lōʻihi lōʻihi;
- polyps , protesserances ma ka ihu;
- nā maʻi maʻamau o ka'ōpū hanu me nā manawa pinepine;
- me ka lawaʻole o ka hanuʻana;
- hoʻomau pinepine i ka bronchitis, sinusitis, sinusitis;
- pancreatitis;
- he paʻakikī ikaika, i ka pō, me ka hoʻokuʻuʻana o ka'ōlohelohe a iʻole ka manawalehua;
- nā maʻi o ka'ōpū a me nā'ōpū;
- ka cholecystitis mau;
- ka hanu o ka hanu , nā hōʻeha hānō;
- nā maʻi o ka pūnaha genitarianinary, impotence.
ʻO nā hōʻailona i kākauʻia o cystic fibrosis e pili ana i kaʻikeʻole o kaʻehaʻeha i ka kino e huahua i kahi pilikino e pili ana i keʻano kūlohelohe o ka metabolism wai-electrolyte ma nā pū o nā'ōpū o loko. ʻO kēia ka hopena i ka piʻiʻana o ka māmā a me ka viscosity o ka wai i hanaʻia e ka nui o nā poho o ka hoʻonā i loko. Hoʻonuiʻia ka hanana, e ulu ana ka huapili, a hiki ke hoʻololi i nā loli i loko o nā'ōpū, i loko o ka maʻi.
ʻO keʻano'ōpū o cystic fibrosis kahi i hōʻikeʻia e ke koko, ke kuʻi, ka paʻa a me ka luaʻiʻana. ʻO kēia mau hōʻailona ke hiki ke mālama i ka lāʻau ma ka laweʻana i nā lāʻau lapaʻau me nā enzymes, akā e hoʻomau mau ana nā hanana pulmonary o ka maʻi.
Cybio Fibrosis - Kaʻike
ʻO ka mea mua, ua nānāʻia kaʻike o nā hōʻailonaʻoi loa o ka maʻi - ka viscosity o ka mea huna o nā'ōlohelohe i loko, ka exacerbation o nā maʻi mau loa o ka'ōpū hanu. Ma hope o kēia, pono e hoʻokū i ka nohoʻana o nā hua male mai nā mākua mai a nānā i nā hihia o ka pōʻino ma kaʻohana.
ʻO ka kānana pono loa no ka cystic fibrosis he DNA. ʻO kēia ho'āʻo ka mea maʻalahi, a hiki ke hanaʻia ma loko o ka'ōpū ma ka nānāʻana i ka wai amniotic. ʻO ka helu o nā hopena hoʻopunipuniʻaʻoleʻoi aku ma mua o 3% a hiki iāʻoe keʻike kokeʻia me kaʻole o nā mea hou.
ʻO ka hoʻoholoʻana i ka nui o nā mea momona a me ka chymotrypsin i loko o ka waihona o ka mea maʻi keʻano hoʻokahi o ka hana eʻike ai i ka maʻi. Hoʻonohonohoʻia nā haʻawina maʻamau o nā chymotrypsin ma kēlā me kēia maʻamau. ʻO ka nui o nā meaʻona e ho'āla i ka hilinaʻi o cystic fibrosis ma mua o 20-25 mmol i ka lā.
ʻO kahi ho'āʻo wela no cystic fibrosis me pilocarpine he haʻawina ia o ke kaʻina o ka chlorides i loko o ka wai i hunaʻia e nā pores. Pono e ho'āʻoʻia ka ho'āʻoʻana iʻekolu manawa e hoʻopaʻa i ka hōʻailona pololei.